Thursday 26 May 2022 10:01 PM Woman who suffers from rare 'maple syrup urine disease' says that she may DIE ... trends now
A woman who suffers from the rare 'maple syrup urine disease' says that the formula shortage striking much of the nation may kill her.
Hannah Dolins, 28, requires specialized metabolic formula at every meal in order to live, as her condition prevents her body from properly breaking down proteins in other food.
She goes through around three cases of Ketonex-2 formula every month, but because of nationwide supply shortages she has not been able to purchase a new case for three months now.
Her supplies are dwindling, and she tells Insider that she fear the shortage will lead to death. A recent COVID-19 infection she has suffered has only made matters worse as well.
While she is an adult, many parents around the country are telling similar tales of how these recent shortages have placed them in a spot where they worry how they can feed their baby every day.
Hannah Dolins (pictured), 28, suffers from a rare condition called maple syrup urine disease, that requires her to consume metabolic formula every day
Dolins (pictured) warns that she may die if she runs out of formula amid a nationwide shortage
'I'm 28 years old. I am not ready to die. But without my specialized metabolic formula, Ketonex-2, I may die. I need my formula to live,' she wrote in a first person essay.
She notes that the rare condition only affects around 2,000 people in the U.S. every year.
It has the 'maple syrup' moniker because those who suffer from it often have sweet smelling urine.
The condition prevents her body from breaking down amino acids, minerals and vitamins in many common foods.
Dolins says that if she does not receive the formula for 24 to 48 hours then her brain will begin to deteriorate and she will likely fall into a coma and die.
I want the country to know that when I run out of Ketonex-2, hospitalization will be the only way to keep me alive, but it's a short-term solution that probably won't save my
